Nabyta choroba torbielowata nerek towarzysząca rakowi nerkowokomórkowemu

Kod Orpha: 404514Kod OMIM:

Definicja

A rare subtype of renal cell carcinoma, ocurring in the context of end-stage kidney disease and acquired cystic kidney disease, characterized by a usually well circumscribed, solid, multifocal, bilateral tumor with inter- or intracellular microlumen formation (leading to cribiform architecture). Tumors are often diagnosed incidentally in early stages, although complications caused by renal cysts (dull flank or abdominal pain, fever) or renal parenchymal bleeding may mask the underlying neoplastic process. Most have an indolent behavior.

Dane
Klasyfikacja

Choroba

Kod ORPHA
404514
Kod OMIM
-
Kod ICD10
C64
Kod ICD11
-

Brak opisu rozszerzonego dla tej choroby. Opracowanie w toku.

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