Mięsak maziówkowy

Kod Orpha: 3273Kod OMIM: 300813

Definicja

Synovial sarcoma is an aggressive soft tissue sarcoma (see this term), occurring most commonly in adolescents and young adults (15 to 40 years), usually localized near the large joints of the extremities but also in the head and neck, mediastinum and viscera (lung, kidney etc), clinically presenting as a deep seated swelling or a painful mass often with an initial indolent course and is characterized by its local invasiveness and a propensity to metastasize. The origin of synovial sarcoma is likely from multipotent mesenchymal cells and not synovium (contrary to its name).

Dane
Klasyfikacja

Choroba

Synonimy
Synovialosarcoma
Kod ORPHA
3273
Kod OMIM
300813
Kod ICD10
C49.9
Kod ICD11
-

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