Rak śluzowo-cewkowy i wrzecionowatokomórkowy

Kod Orpha: 319322Kod OMIM:

Definicja

Mucinous tubular and spindle cell renal carcinoma is a rare subtype of renal cell carcinoma characterized, histologically, by tubular architecture and sheets of spindle cells embedded in a mucinous/myxoid stroma and, macroscopically, by a solid, generally well-circumscribed, partially encapsulated tumor of variable size, with a homogenously colored, bulging cut surface, occassionally containing areas of hemorrhage or necrosis, usually located in the cortex. Patients can present abdominal/flank pain, adbominal mass and/or hematuria, however most are asymptomatic and tumor is discovered incidentally. Indolent behavior is frequent and association with nephrolithiasis and end-stage kidney disease has been noted.

Dane
Klasyfikacja

Choroba

Kod ORPHA
319322
Kod OMIM
-
Kod ICD10
C64
Kod ICD11
-

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