Wtórny zespół hipereozynofilowy

Kod Orpha: 314962Kod OMIM:

Definicja

A rare hypereosinophilic syndrome characterized by hypereosinophilia produced by reactive/non-clonal eosinophils secondary to an underlying medical condition and persisting for at least six months. The disorder can derive from non-neoplastic conditions (such as chronic infections and infestations, allergic reactions, intoxications, or autoimmune and chronic inflammatory disorders) or from neoplasms including non-myeloid malignancies, among others. It is associated with signs of organ infiltration, dysfunction, and damage. Clinical manifestations are highly variable, depending on the organ systems involved, and most commonly include dermatologic, pulmonary, cardiac, gastrointestinal, and cerebral manifestations.

Dane
Klasyfikacja

Choroba

Synonimy
HES-R
HES-R
Reaktywny zespół hipereozynofilowy
Wtórny HES
Reactive hypereosinophilic syndrome
Secondary HES
Kod ORPHA
314962
Kod OMIM
-
Kod ICD10
D47.5
Kod ICD11
-

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