Naczyniakowłókniak młodzieńczy nosogardła

Kod Orpha: 289596Kod OMIM:

Definicja

Juvenile nasopharyngeal angiofibroma (JNA) is a rare and benign but locally aggressive fibrovascular tumor arising from the posterolateral wall of the nasopharynx, which affects mainly young and adolescent males (onset usually occurring between 7-19 years of age) and that presents as a mass in the nasopharynx and nasal cavity, leading to manifestations such as nasal obstruction, epistaxis, profound facial swelling, proptosis or diplopia. Although slowly progressive, it has a high rate of recurrence and sometimes invades adjacent structures.

Dane
Klasyfikacja

Choroba

Synonimy
JNA
JNA
Kod ORPHA
289596
Kod OMIM
-
Kod ICD10
D10.6
Kod ICD11
2E90.6

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