Znamię Oty

Kod Orpha: 263425Kod OMIM:

Definicja

Nevus of Ota is an oculodermal melanocytosis more commonly found in Asian and African populations, usually present at birth and characterized by a usually unilateral, bluish gray, patchy, speckled pigmentation (that may progressively enlarge and darken) affecting the skin of the face along the distribution of the ophthalmic and maxillary divisions of the trigeminal nerve (periorbital region, temple, forehead, malar area, nose). In 2/3 cases the ipsilateral sclera is affected. Nevus of Ota usually remains stable once adulthood is reached but an increased risk of glaucoma and uveal melanoma may be observed. Extracutaneous lesions may also occur in cornea, retina, tympanum, nasal mucosa, pharynx, palate. Nevus of Ota occurs as solitary conditions but seldom may occur together with the nevus of Ito or nevus spilus.

Dane
Klasyfikacja

Choroba

Synonimy
Nevus fusculoceruleus ophthalmomaxillaris
Znamię okulodermalne
Kod ORPHA
263425
Kod OMIM
-
Kod ICD10
D22.3
Kod ICD11
LC10

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