Guz brodawkowaty glioneuronalny

Kod Orpha: 251962Kod OMIM:

Definicja

A rare mixed neuronal-glial tumor characterized by a supratentorial space-occupying lesion in periventricular location, often with prominent cystic change. The histological hallmark of this low-grade neoplasm is its pseudopapillary appearance with a single layer of cuboidal cells around hyalinized blood vessels, associated with sheets or focal collections of neuronal cells. Clinical presentation is variable and non-specific, most frequently with headache and seizures. Prognosis is favorable after complete resection.

Dane
Klasyfikacja

Choroba

Synonimy
PGNT
PGNT
Pseudopapillary ganglioglioneurocytoma
Pseudopapillary neurocytoma with glial differentiation
Pseudopapillary ganglioglioneurocytoma
Pseudopapillary neurocytoma with glial differentiation
Kod ORPHA
251962
Kod OMIM
-
Kod ICD10
D33.0
Kod ICD11
2A00.21

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