Glejakowatość mózgu

Kod Orpha: 251582Kod OMIM:

Definicja

A rare glial tumor characterized by extensive infiltration of the brain, often extending to infratentorial structures and even the spinal cord. The tumor corresponds to WHO grade III and is composed of elongated glial cells typically resembling astrocytes. Cases in which the predominant cell type is oligodendroglial have also been described. Some tumors develop a circumscribed neoplastic mass in addition to the diffuse lesion, usually showing features of high-grade glioma. Clinical symptoms include dementia, headache, seizures, signs of increased intracranial pressure, and a variety of neurological deficits. Prognosis is generally poor.

Dane
Klasyfikacja

Choroba

Kod ORPHA
251582
Kod OMIM
-
Kod ICD10
C71.0
Kod ICD11
2A00.0Y

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