Zespół Evansa

Kod Orpha: 1959Kod OMIM:

Definicja

A rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

Dane
Klasyfikacja

Choroba

Synonimy
Autoimmune hemolytic anemia and autoimmune thrombocytopenia
Autoimmunologiczna niedokrwistość hemolityczna i autoimmunologiczna trombocytopenia
Pancytopenia immunologiczna
Immune pancytopenia
Kod ORPHA
1959
Kod OMIM
-
Kod ICD10
D69.3
Kod ICD11
3A20.5

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