Przetoka/torbiel grzbietu nosa

Kod Orpha: 141219Kod OMIM:

Definicja

A rare otorhinolaryngological malformation characterized by the presence of a dermoid cyst, located on the dorsum of the nose, which presents a fistula, often extending to the intracranial region. Patients present a firm, slow-growing mass, which contains skin and dermal elements (including hair follicles and sebaceous glands), that do not transilluminate or compress, and may be associated with intermittent or chronic discharge of sebaceous material, soft tissue and skeletal deformity, and local infection. Meningitis, convulsions and cerebral abscess may be observed if intracranial extension exists.

Dane
Klasyfikacja

Wada morfologiczna

Kod ORPHA
141219
Kod OMIM
-
Kod ICD10
Q18.8
Kod ICD11
LA5Y

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