Definition
A rare inherited connective tissue disorder characterized by skin hyperextensibility, widened atrophic scars, and generalized joint hypermobility.
Definition
A rare inherited connective tissue disorder characterized by skin hyperextensibility, widened atrophic scars, and generalized joint hypermobility.
Disease data
Classification
Disease
Synonyms
Classical EDS
EDS, typ klasyczny
cEDS
ORPHA code
287
OMIM code
130000
ICD10 code
Q79.6
ICD11 code
LD28.10
No additional description.
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