Congenital pulmonary lymphangiectasia

Orpha code: 2414OMIM code: 265300

Definition

A rare developmental disorder involving the lung and characterized by pulmonary subpleural, interlobar, perivascular, and peribronchial lymphatic dilatation.

Disease data
Classification

Disease

Synonyms
Pulmonary lymphangiomatosis
Limfangiomatoza płucna
ORPHA code
2414
OMIM code
265300
ICD10 code
Q33.8
ICD11 code
LA75.Y

No additional description.

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