Paroxysmal nocturnal hemoglobinuria

Orpha code: 447OMIM code: 615399

Definition

Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterized by corpuscular hemolytic anemia, bone marrow failure and frequent thrombotic events.

Disease data
Classification

Disease

Synonyms
Choroba Marchiafava i Micheli
Marchiafava-Micheli disease
PNH
PNH
ORPHA code
447
OMIM code
615399
ICD10 code
D59.5
ICD11 code
3A21.0

No additional description.

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