Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A form of pulmonary arterial hypertension (PAH) characterized by elevated pulmonary arterial resistance leading to right heart failure; it is progressive and potentially fatal. The majority cases have an identifiable genetic cause, but a significant proportion are idiopathic. Disease data Classification Disease Synonyms Idiopathic and/or familial pulmonary arterial hypertension ORPHA code 422 OMIM code 615344 ICD10 code I27.0 ICD11 code BB01.0 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl