Dermatitis herpetiformis

Orpha code: 1656OMIM code: 601230

Definicja

A chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. It may also appear as a consequence of gluten intolerance.

Disease data
Klasyfikacja

Disease

Synonimy
Duhring-Brocq disease
Choroba Durhinga i Brocqa
Kod ORPHA
1656
Kod OMIM
601230
Kod ICD10
L13.0
Kod ICD11
EB44

No additional description.

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