Definition
Best vitelliform macular dystrophy (BVMD) is a genetic macular dystrophy characterized by loss of central visual acuity, metamorphopsia and a decrease in the Arden ratio secondary to an egg yolk-like lesion located in the foveal or parafoveal region.
Definition
Best vitelliform macular dystrophy (BVMD) is a genetic macular dystrophy characterized by loss of central visual acuity, metamorphopsia and a decrease in the Arden ratio secondary to an egg yolk-like lesion located in the foveal or parafoveal region.
Disease data
Classification
Disease
Synonyms
BMD
BMD
BVMD
Choroba Besta
Dystrofia plamki Besta
Dystrofia plamki żółtej o początku w wieku młodzieńczym
Dystrofia plamki żółtej o wczesnym początku
Dystrofia plamki żółtej typu 2
Polimorficzne zwyrodnienie plamki żółtej
BVMD
Best disease
Best macular dystrophy
Early-onset vitelliform macular dystrophy
Juvenile-onset vitelliform macular dystrophy
Polymorphic vitelline macular degeneration
Vitelliform macular dystrophy type 2
ORPHA code
1243
OMIM code
153700
ICD10 code
H35.5
ICD11 code
9B70
No additional description.
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