Autosomal dominant Kenny-Caffey syndrome

Orpha code: 93325OMIM code: 127000

Definicja

A rare, primary bone dysplasia characterized by severe growth retardation, short stature, cortical thickening and medullary stenosis of long bones, delayed closure of the anterior fontanelle, absent diploic space in the skull bones, prominent forehead, macrocephaly, dental anomalies, eye problems (hypermetropia and pseudopapilledema), and hypocalcemia due to hypoparathyroidism, sometimes resulting in convulsions. Intelligence is normal.

Disease data
Klasyfikacja

Etiological subtype

Kod ORPHA
93325
Kod OMIM
127000
Kod ICD10
Q87.1
Kod ICD11
-

No additional description.

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