Paraneoplastic pemphigus

Orpha code: 63455OMIM code:

Definition

A rare form of autoimmune bullous skin disease characterized by polyformative skin lesions, typically beginning on the oral mucus membranes, and generally associated with lymphoma or chronic lymphoid leukemia.

Disease data
Classification

Disease

ORPHA code
63455
OMIM code
-
ICD10 code
L10.8
ICD11 code
EB40.2

No additional description.

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