Pleomorphic salivary gland adenoma

Orpha code: 454821OMIM code: 181030

Definition

A rare tumor of salivary glands characterized by a benign, well-circumscribed, slow-growing, painless mass most commonly occurring in the parotid gland (but also the palate, submandibular gland, or nasal septal mucosa), histopathologically composed of epithelial and myoepithelial / stromal components. Possible signs and symptoms depend on the location of the tumor and include facial nerve weakness, mild dysphagia, or unilateral nasal obstruction. Recurrence rates are low, although tumor rupture and spillage have been reported. Malignant transformation may occur in a small percentage of cases.

Disease data
Classification

Histopathological subtype

ORPHA code
454821
OMIM code
181030
ICD10 code
D11.0
ICD11 code
-

No additional description.

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