Mucinous cystadenocarcinoma of the pancreas

Orpha code: 424053OMIM code:

Definition

A rare, epithelial tumor of the pancreas characterized, histologically, by columnar, mucin-producing epithelium associated with ovarian-type subepithelial stroma, which does not communicate with the pancreatic ductal system, most frequently localized to the body or tail of the pancreas. Clinically, small tumors (<3 cm) are usually asymptomatic, while large tumors typically present obstructive jaundice, a palpable abdominal mass, and may associate portal hypertension, hemobilia and diabetes mellitus.

Disease data
Classification

Disease

Synonyms
Pancreatic mucinous cystadenocarcinoma
Pancreatic mucinous cystadenocarcinoma
ORPHA code
424053
OMIM code
-
ICD10 code
C25.7
ICD11 code
-

No additional description.

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