Ocular cystinosis

Orpha code: 411641OMIM code: 219750

Definition

Ocular cystinosis is the benign, adult form of cystinosis (see this term), a metabolic disease characterized by an accumulation of cystine crystals in the cornea and conjunctiva responsible for tearing and photophobia and associated with no other additional manifestations.

Disease data
Classification

Clinical subtype

Synonyms
Adult-onset cystinosis
Cystynoza nienefropatyczna
Cystynoza o początku w wieku dorosłym
Non-nephropathic cystinosis
ORPHA code
411641
OMIM code
219750
ICD10 code
E72.0
ICD11 code
-

No additional description.

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