Necrotizing enterocolitis

Orpha code: 391673OMIM code:

Definition

A rare intestinal disease characterized by potentially life-threatening inflammatory bowel necrosis predominantly affecting preterm neonates. Patients may present with feeding intolerance, lethargy, temperature instability, abdominal distention, blood-stained stools, diarrhea, bilious vomiting, apnea, and signs of sepsis. Radiographic features include pneumatosis intestinalis, portal venous gas, presence of fixed, dilated intestinal loops, bowel wall edema, and (in case of bowel perforation) pneumoperitoneum.

Disease data
Classification

Disease

ORPHA code
391673
OMIM code
-
ICD10 code
P77
ICD11 code
KB88

No additional description.

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