Dermatofibrosarcoma protuberans

Orpha code: 31112OMIM code: 607907

Definition

Dermatofibrosarcoma protuberans (DFSP) is a rare infiltrating soft tissue sarcoma, generally of low grade malignancy, arising from the dermis of the skin and characteristically associated with a specific chromosomal translocation t(17;22).

Disease data
Classification

Disease

Synonyms
DFSP
DFSP
ORPHA code
31112
OMIM code
607907
ICD10 code
C49.9
ICD11 code
-

No additional description.

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