Neurenteric cyst

Orpha code: 268865OMIM code:

Definicja

A rare, congenital, non-syndromic malformation of neurenteric canal, spinal cord and column, characterized by intraspinal, predominantly intradural-extramedullary cystic mass located typically ventral to the spinal cord. Histopathology reveals columnar or cuboidal epithelium with or without cilia and mucus globules. Patients may be asymptomatic or present with signs and symptoms of compression of the spinal cord and associated nerve roots, such as focal weakness, progressive paresis, paresthesias, gait disturbance, or radicular pain. Concomitant congenital vertebral anomalies are frequently observed.

Disease data
Klasyfikacja

Morphological anomaly

Kod ORPHA
268865
Kod OMIM
-
Kod ICD10
Q06.8
Kod ICD11
LA07.Y

No additional description.

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