Microcephalic osteodysplastic primordial dwarfism type II

Orpha code: 2637OMIM code: 210720

Definition

A rare bone disease and a form of microcephalic primordial dwarfism characterized by severe pre- and postnatal growth retardation, with marked microcephaly in proportion to body size, skeletal dysplasia, abnormal dentition, insulin resistance, and increased risk for cerebrovascular disease.

Disease data
Classification

Malformation syndrome

Synonyms
MOPD type II
MOPD typu II
Pierwotna karłowatość osteodysplastyczna Majewskiego typu II
Majewski osteodysplastic primordial dwarfism type II
ORPHA code
2637
OMIM code
210720
ICD10 code
Q87.1
ICD11 code
-

No additional description.

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