Hartnup disease

Orpha code: 2116OMIM code: 234500

Definition

A rare metabolic disorder belonging to the neutral aminoacidurias, mainly characterized by skin photosensitivity, ocular and neuropsychiatric features, due to abnormal renal and gastrointestinal transport of neutral amino acids (tryptophan, alanine, asparagine, glutamine, histidine, isoleucine, leucine, phenylalanine, serine, threonine, tyrosine and valine).

Disease data
Classification

Disease

Synonyms
Aminoaciduria, Hartnup type
Aminoaciduria typu Hartnupów
Choroba Hartnupów
Hartnup disorder
ORPHA code
2116
OMIM code
234500
ICD10 code
E72.0
ICD11 code
5C60.Y

No additional description.

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