Familial developmental dysphasia

Orpha code: 1799OMIM code: 600117

Definition

Familial developmental dysphasia is a severe form of developmental verbal apraxia characterized by a deficit in spontaneous speech, writing, grammatical judgment and repetition, defective articulation, moderate to severe degree of dyspraxia, a reduced use of consonant clusters, and comprehension delay. Hearing and intelligence are normal.

Disease data
Classification

Clinical syndrome

Synonyms
Billard-Toutain-Maheut syndrome
Dysfazja związana z FOXP2
Zespół Billarda, Toutaina i Maheuta
FOXP2-associated dysphasia
ORPHA code
1799
OMIM code
600117
ICD10 code
F80.1
ICD11 code
-

No additional description.

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