Familial idiopathic dilatation of the right atrium

Orpha code: 1677OMIM code:

Definition

A rare congenital heart malformation of unknown etiology that is characterized by an extremely dilated right atrium, and that is usually asymptomatic and fortuitously discovered by echocardiography or chest radiography, and can be sometimes associated with other anomalies such as atrial arrhythmias (e.g. atrial flutter, atrial fibrillation, supraventricular tachycardia), severe tricuspid regurgitation, or atrial thrombus that could lead to potentially life-threatening thromboembolic complications.

Disease data
Classification

Morphological anomaly

ORPHA code
1677
OMIM code
-
ICD10 code
Q20.8
ICD11 code
-

No additional description.

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