Castleman disease

Orpha code: 160OMIM code: 148000

Definition

A benign lymphoproliferative disorder that may present as a localized or multicentric form. The clinical manifestations are heterogeneous, ranging from asymptomatic discrete lymphadenopathy to recurrent episodes of diffuse lymphadenopathy with severe systemic symptoms.

Disease data
Classification

Disease

Synonyms
Angiofollicular ganglionic hyperplasia
Angiofollicular ganglionic hyperplasia
Naczyniowogrudkowy przerost węzłów chłonnych
Angiofollicular lymph hyperplasia
ORPHA code
160
OMIM code
148000
ICD10 code
D47.7
ICD11 code
4B2Y

No additional description.

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