Wrodzona sekwestracja płuc

Kod Orpha: 3161Kod OMIM:

Definicja

Congenital pulmonary sequestration is a rare respiratory malformation characterized by a cystic or solid mass of nonfunctioning primitive segmental lung tissue that does not communicate with the tracheobronchial tree and has anomalous systemic blood supply. Intralobar pulmonary sequestration may be asymptomatic or may present with recurrent pulmonary infections, hemoptysis, chest pain, cough and is usually diagnosed in older children and adults. Extralobar pulmonary sequestration present with respiratory distress, cyanosis, difficulty feeding or infection, may be associated with other anomalies and is mostly diagnosed in neonates or infants.

Dane
Klasyfikacja

Zespół wad wrodzonych

Synonimy
Congenital bronchopulmonary sequestration
Wrodzona sekwestracja oskrzelowo-płucna
Kod ORPHA
3161
Kod OMIM
-
Kod ICD10
Q33.2
Kod ICD11
LA75.6

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