Essential iris atrophy

Definition

A clinical variant of iridocorneal endothelial (ICE) syndrome, characterized by progressive iris atrophy and holes present on the surface of the iris, corneal edema, corectopia, uveal ectropion and anterior synechiae. Secondary glaucoma is also a common complication of the disease.

Disease data

Classification

Clinical subtype

ORPHA code

98981

OMIM code

ICD10 code

H21.2

ICD11 code

9A90.2

*Soruce