Melanoma of soft tissue

Orpha code: 97338OMIM code:

Definition

A rare soft tissue tumor characterized by a slowly growing mass typically involving tendons and aponeuroses of the extremities, composed of polygonal or spindle-shaped cells with melanocytic differentiation. The tumor typically affects young adults, who often present with pain or tenderness at the tumor site. Prognosis is poor with high recurrence rates and frequent metastasis, especially to lymph nodes, lung, and bones.

Disease data
Classification

Disease

Synonyms
Clear cell sarcoma of the tendons and aponeuroses
Mięsak jasnokomórkowy ścięgien i powięzi
Mięsak jasnokomórkowy tkanek miękkich
ORPHA code
97338
OMIM code
-
ICD10 code
C43.7
ICD11 code
-

No additional description.

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