Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare soft tissue tumor characterized by a slowly growing mass typically involving tendons and aponeuroses of the extremities, composed of polygonal or spindle-shaped cells with melanocytic differentiation. The tumor typically affects young adults, who often present with pain or tenderness at the tumor site. Prognosis is poor with high recurrence rates and frequent metastasis, especially to lymph nodes, lung, and bones. Disease data Classification Disease Synonyms Clear cell sarcoma of the tendons and aponeuroses Mięsak jasnokomórkowy ścięgien i powięzi Mięsak jasnokomórkowy tkanek miękkich ORPHA code 97338 OMIM code - ICD10 code C43.7 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl