Severe immune-mediated enteropathy

Orpha code: 94075OMIM code:

Definicja

Severe-immune mediated enteropathy describes a variety of intestinal disorders that can range from a serious, early-onset systemic disease (IPEX; see this term) to a mild isolated gastrointestinal disease. In children it manifests with severe diarrhea and dehydration in the presence of characteristic antibodies (anti-enterocyte and anti-goblet cell) and in adults with chronic diarrhea, malabsorption and weight loss.

Disease data
Klasyfikacja

Category

Synonimy
Autoimmune enteropathy
Enteropatia autoimmunologiczna
Przewlekła biegunka dziecięca o podłożu immunologicznym
Immune-mediated protracted diarrhea of infancy
Kod ORPHA
94075
Kod OMIM
-
Kod ICD10
-
Kod ICD11
-

No additional description.

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