Transient pseudohypoaldosteronism

Orpha code: 93164OMIM code:

Definition

A rare renal tubulopathy secondary to urinary tract infection (UTI) and/or urinary tract malformation (UTM) characterized by renal tubular resistance to aldosterone, characterized by hyponatremia, metabolic acidosis, hyperkalemia and inappropriately high serum aldosterone concentration and clinically manifesting as dehydration, vomiting, and poor oral intake.

Disease data
Classification

Disease

Synonyms
Secondary pseudohypoaldosteronism
TPHA
TPHA
ORPHA code
93164
OMIM code
-
ICD10 code
N15.8
ICD11 code
-

No additional description.

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