Transient pseudohypoaldosteronism

Orpha code: 93164OMIM code:

Definicja

A rare renal tubulopathy secondary to urinary tract infection (UTI) and/or urinary tract malformation (UTM) characterized by renal tubular resistance to aldosterone, characterized by hyponatremia, metabolic acidosis, hyperkalemia and inappropriately high serum aldosterone concentration and clinically manifesting as dehydration, vomiting, and poor oral intake.

Disease data
Klasyfikacja

Disease

Synonimy
Secondary pseudohypoaldosteronism
TPHA
TPHA
Kod ORPHA
93164
Kod OMIM
-
Kod ICD10
N15.8
Kod ICD11
-

No additional description.

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