Congenital megacalycosis

Definition

Congenital megacalycosis is a rare renal malformation, characterized by non-obstructive dilation of the renal calyces as well as an increased calyceal number (12-20), with a normal renal pelvis, ureter, and bladder. It may be unilateral or bilateral and is usually asymptomatic unless complicated by nephrolithiasis and urinary tract infection.

Disease data

Classification

Morphological anomaly

ORPHA code

93109

OMIM code

ICD10 code

Q63.8

ICD11 code

*Soruce