Secondary intestinal lymphangiectasia

Orpha code: 90363OMIM code:

Definition

Secondary intestinal lymphangiectasia is an acquired from of intestinal lymphangiectasia (see this term) manifesting as a protein-losing enteropathy due to another disorder such as Crohn’s disease, congestive heart failure, sarcoidosis, Turner syndrome (see these terms) and often in patients who have undergone a Fontan operation. It is characterized by malabsorption, diarrhea, edema due hypoproteinemia, steatorrhea and serosal effusions.

Disease data
Classification

Disease

ORPHA code
90363
OMIM code
-
ICD10 code
I89.0
ICD11 code
-

No additional description.

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