Lupus erythematosus panniculitis

Orpha code: 90285OMIM code:

Definition

A rare form of chronic cutaneous lupus erythematosus characterized by recurrent, indurated, erythematous plaques and subcutaneous nodules with normal overlying epidermis, occurring predominantly on the face, upper arms, trunk, buttocks, and thighs. The lesions can ulcerate and lead to scarring. Histological findings include lobular lymphocytic panniculitis, hyaline fat necrosis, mucin deposition, and calcification. The condition may be associated with discoid or systemic lupus erythematosus.

Disease data
Classification

Disease

Synonyms
Lupus erythematosus profundus
Lupus erythematosus profundus
ORPHA code
90285
OMIM code
-
ICD10 code
L93.2
ICD11 code
EB51.Y

No additional description.

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