Primary cutaneous peripheral T-cell lymphoma not otherwise specified

Orpha code: 86885OMIM code:

Definition

An extremely rare, primary cutaneous T-cell lymphoma disorder characterized by solitary, or multifocal and diffuse, cutaneous lesions, ranging from tumor-like patches, plaques, papules, nodules, and/or erythroderma, located on any area of the body, which rapidly progress and may become ulcerated and/or infected. Systemic involvement may be associated.

Disease data
Classification

Disease

Synonyms
Primary cutaneous peripheral T-cell lymphoma NOS
Pierwotny skórny chłoniak z obwodowych komórek T NOS
Primary cutaneous unspecified peripheral T-cell lymphoma
ORPHA code
86885
OMIM code
-
ICD10 code
C84.4
ICD11 code
2A90.C

No additional description.

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