X-linked severe congenital neutropenia

Orpha code: 86788OMIM code: 300299

Definicja

X-linked severe congenital neutropenia is an immunodeficiency syndrome characterized by recurrent major bacterial infections, severe congenital neutropenia, and monocytopenia. It has been described in five males spanning three generations of one family. It is transmitted as an X-linked recessive trait and is caused by mutations in the <i>WAS</i> gene, encoding the WASP protein.

Disease data
Klasyfikacja

Disease

Kod ORPHA
86788
Kod OMIM
300299
Kod ICD10
D70
Kod ICD11
-

No additional description.

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