Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A group of rare renal diseases, characterized by amyloid fibril deposition of apolipoprotein A-I or A-II (AApoAI or AApoAII amyloidosis), lysozyme (ALys amyloidosis) or fibrinogen A-alpha chain (AFib amyloidosis) in one or several organs. Renal involvement leading to chronic renal disease and renal failure is a common sign. Additional manifestations depend on the organ involved and the type of amyloid fibrils deposited. Disease data Classification Disease Synonyms Amyloidosis, Ostertag type Amyloidoza, typ Ostertaga Dziedziczna amyloidoza nerek Dziedziczna nefropatia amyloidowa Rodzinna amyloidoza nerkowa Rodzinna nefropatia amyloidowa Familial amyloid nephropathy Familial renal amyloidosis Hereditary amyloid nephropathy Hereditary renal amyloidosis ORPHA code 85450 OMIM code 105200 ICD10 code E85.0 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl