Smith-Magenis syndrome

Orpha code: 819OMIM code: 182290

Definition

A rare, genetic, neurodevelopmental disorder characterized by cognitive impairment of variable severity, behavioral abnormalities, and sleep disturbance. Patients present with distinctive physical features and a wide range of malformations (e.g. cardiac, renal).

Disease data
Classification

Malformation syndrome

Synonyms
17p11.2 microdeletion syndrome
Zespół mikrodelecji 17p11.2
ORPHA code
819
OMIM code
182290
ICD10 code
Q93.5
ICD11 code
LD44.H1

No additional description.

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