Oculocutaneous albinism type 1A

Orpha code: 79431OMIM code: 203100

Definition

A severe form of oculocutaneous albinism type 1 (OCA1) characterized by complete absence of melanin and manifesting as white hair and skin, blue, fully translucent irises, nystagmus and misrouting of the optic nerves.

Disease data
Classification

Clinical subtype

Synonyms
OCA1A
Albinizm oczno-skórny tyrozynazo-ujemny
OCA1A
Tyrosinase-negative oculocutaneous albinism
ORPHA code
79431
OMIM code
203100
ICD10 code
E70.3
ICD11 code
-

No additional description.

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