Central areolar choroidal dystrophy

Orpha code: 75377OMIM code: 613144

Definition

A hereditary macular disorder, usually presenting between the ages of 30-60, characterized by a large area of atrophy in the centre of the macula and the loss or absence of photoreceptors, retinal pigment epithelium and choriocapillaris in this area, resulting in a progressive decrease in visual acuity.

Disease data
Classification

Disease

Synonyms
Areolar atrophy of the macula
CACD
Centralne otoczkowe stwardnienie błony naczyniowej
Otoczkowa atrofia plamki
CACD
Central areolar choroidal sclerosis
ORPHA code
75377
OMIM code
613144
ICD10 code
H31.2
ICD11 code
9B61

No additional description.

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