Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare genetic disease characterized by the triad of adult-onset moderate to severe bilateral sensorineural hearing loss, premature graying of scalp hair, and essential tremor manifesting as involuntary shaking of the head. Additional pigmentation abnormalities have not been reported in this syndrome. Disease data Classification Disease Synonyms Sensorineural deafness-early graying-essential tremor syndrome Sensorineural deafness-early graying-essential tremor syndrome ORPHA code 66633 OMIM code - ICD10 code H90.3 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl