Incomplete septal cirrhosis

Orpha code: 596941OMIM code:

Definition

A histopathological form of portosinusoidal vascular disease characterized by the presence of incomplete, thin, perforated, or blind-ended septa, which intermittently delimit rudimentary nodules, although complete cirrhotic-type regenerative nodules are not seen. Isolated collagen bundles can also be observed within the parenchyma.

Disease data
Classification

Histopathological subtype

Synonyms
Incomplete septal fibrosis
Incomplete septal fibrosis
ORPHA code
596941
OMIM code
-
ICD10 code
K74.6
ICD11 code
-

No additional description.

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