Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Familial Hemophagocytic lymphohistiocytosis (FHL) is a rare primary immunodeficiency characterized by a macrophage activation syndrome (see this term) with an onset usually occurring within a few months or less common several years after birth. Disease data Classification Disease Synonyms Familial HLH Rodzinna HLH ORPHA code 540 OMIM code 618998 ICD10 code D76.1 ICD11 code 4A01.23 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl