Familial hemophagocytic lymphohistiocytosis

Orpha code: 540OMIM code: 618998

Definicja

Familial Hemophagocytic lymphohistiocytosis (FHL) is a rare primary immunodeficiency characterized by a macrophage activation syndrome (see this term) with an onset usually occurring within a few months or less common several years after birth.

Disease data
Klasyfikacja

Disease

Synonimy
Familial HLH
Rodzinna HLH
Kod ORPHA
540
Kod OMIM
618998
Kod ICD10
D76.1
Kod ICD11
4A01.23

No additional description.

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