Primary central nervous system lymphoma

Orpha code: 46135OMIM code:

Definition

Primary central nervous system lymphoma (PCNSL) is a rare nervous system tumor, predominantly due to diffuse large B-cell lymphoma, that involves brain, leptomeninges, eyes, or rarely spinal cord, in the absence of systemic diffusion at the time of diagnosis. It is characterized by a solitary tumor that, depending on its location, can lead to a variety of symptoms such as headache, nausea, vomiting (and other signs of raised intracranial pressure), focal neurologic deficits, neuropsychiatric and ocular symptoms, seizures and personality changes.

Disease data
Classification

Disease

Synonyms
PCNSL
PCNSL
Pierwotny chłoniak CUN
Pierwotny chłoniak mózgu
Primary CNS lymphoma
Primary brain lymphoma
ORPHA code
46135
OMIM code
-
ICD10 code
C83.3
ICD11 code
-

No additional description.

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