Proton-pump inhibitor-responsive esophageal eosinophilia

Orpha code: 411696OMIM code:

Definition

Proton-pump inhibitor-responsive esophageal eosinophilia (PPI-REE) is a rare, gastroenterologic disease characterized by typical clinical, endoscopic and histological features of eosinophilic oesophagitis (i.e. symptomatic oesophageal dysfunction associated with eosinophil-predominant mucose infiltrate) which completely remits upon proton pump inhibitor therapy.

Disease data
Classification

Disease

Synonyms
PPI-REE
Eozynofilia przełyku wrażliwa na PPI
PPIRee
PPI-REE
PPI-responsive esophageal eosinophilia
PPIRee
ORPHA code
411696
OMIM code
-
ICD10 code
K20
ICD11 code
-

No additional description.

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