Richieri Costa-Pereira syndrome

Orpha code: 3102OMIM code: 268305

Definition

Richieri Costa-Pereira syndrome is characterized by short stature, Robin sequence, cleft mandible, pre/postaxial hand anomalies (including hypoplastic thumbs), and clubfoot. It has been described in 14 Brazilian families and in one unrelated French patient. Prominent low set ears and a highly arched palate were also observed. Transmission is autosomal recessive.

Disease data
Classification

Malformation syndrome

Synonyms
Short stature-Pierre Robin sequence-cleft mandible-hand anomalies clubfoot syndrome
Niski wzrost - sekwencja Pierre'a Robina - rozszczep żuchwy - wady rąk - stopa końsko-szpotawa
Niski wzrost - zespół Pierre'a Robina - rozszczep żuchwy - wady rąk - stopa końsko-szpotawa
Short stature-Pierre Robin syndrome-cleft mandible-hand anomalies clubfoot syndrome
ORPHA code
3102
OMIM code
268305
ICD10 code
Q87.8
ICD11 code
LD2F.1Y

No additional description.

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