Splenic diffuse red pulp small B-cell lymphoma

Orpha code: 300869OMIM code:

Definition

Splenic diffuse red pulp small B-cell lymphoma is a rare, indolent B-cell non-Hodgkin lymphoma characterized by abnormal proliferation of small, monomorphous, basophilic B-lymphocytes, with villous cytoplasm, in the splenic red pulp, bone marrow and peripheral blood. It typically presents in the late clinical stages with splenomegaly and moderate lymphocytosis. Cytopenias are rare and likely associated with hypersplenism.

Disease data
Classification

Disease

Synonyms
SDRPL
SDRpl
Chłoniak rozlany miazgi czerwonej śledziony
Splenic diffuse red pulp lymphoma
ORPHA code
300869
OMIM code
-
ICD10 code
C83.0
ICD11 code
-

No additional description.

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